Özet:
Hyperimmunoglobulin E syndrome (HIES) is an immunodeficiency
disorder that manifests itself by affecting
more than one system. Arterial aneurysms are among the
significant complications associated with HIES. Surgical
procedures for patients with such aneurysms are uncommon.
In this study, we aim to present the case and
surgical repair of a male child who was previously
diagnosed with HIES and presented with rapidly
expanding ascending aortic aneurysm.
