Demircan, MehmetAksoy, TuğrulCeran Özcan, CananKafkaslı, Ayşe2017-08-152017-08-152008Demircan, M. Aksoy, T. Ceran Özcan, C. Kafkaslı, A. (2008). Tracheal agenesis and esophageal atresia with proximal and distal bronchoesophageal fistulas. Journal of Pediatric Surgery. 43; E1-E3.00223468https://hdl.handle.net/11616/7574Abstract Tracheal agenesis (TA) is an extremely rare, typically fatal congenital tracheal malformation. Lack of prenatal symptoms and emergent presentation usually lead to a failure to arrive at the correct diagnosis and manage the airway properly before the onset of irreversible cerebral anoxia. Esophageal atresia (EA) encompasses a group of congenital anomalies comprising an interruption of the continuity of the esophagus with or without a persistent communication with the trachea. In 86% of cases, there is a distal tracheoesophageal fistula (TEF); in 7%, there is no fistulous connection, whereas in 4%, there is a TEF without atresia. We report the case of an infant born with TA and EA with proximal and distal bronchoesophageal fistulas. During 3 consecutive antenatal ultrasound examinations, there had been polyhydramniosis, difficulty visualizing the stomach, and dilatation of proximal esophagus, leading to a presumptive diagnosis of EA. The clinical presentation, embryology, classification, and surgical management are discussed.eninfo:eu-repo/semantics/openAccessTracheal agenesisEsophageal atresiaPrenatal diagnosisTracheoesophageal fistulaBronchoesophageal fistulaTracheal reconstructionArticle43E1E310.1016/j.jpedsurg.2008.04.015