Abstract:
9-year-old boy presented with a history of lower respiratory infections and
stridor. At age 18 months, he had undergone surgery for inguinal hernia
and tracheoesophageal fistula. Physical examination now revealed a pulsatile
mass in the right supraclavicular region.
Transthoracic echocardiography and aortography showed a right cervical aortic
arch: the right subclavian artery and right carotid artery arose from the right cervical
arch (Fig. 1), and the left carotid artery originated from the ascending aorta
(Fig. 2). Computed tomography revealed this anatomic configuration and tracheal
compression (Figs. 3 and 4). The patient was referred for cardiac surgery.
