Tracheal agenesis and esophageal atresia with proximal and distal bronchoesophageal fistulas
Yükleniyor...
Dosyalar
Tarih
2008
Dergi Başlığı
Dergi ISSN
Cilt Başlığı
Yayıncı
Journal of Pediatric Surgery
Erişim Hakkı
info:eu-repo/semantics/openAccess
Özet
Abstract Tracheal agenesis (TA) is an extremely rare, typically fatal congenital tracheal malformation.
Lack of prenatal symptoms and emergent presentation usually lead to a failure to arrive at the correct
diagnosis and manage the airway properly before the onset of irreversible cerebral anoxia. Esophageal
atresia (EA) encompasses a group of congenital anomalies comprising an interruption of the continuity
of the esophagus with or without a persistent communication with the trachea. In 86% of cases, there is a
distal tracheoesophageal fistula (TEF); in 7%, there is no fistulous connection, whereas in 4%, there is a
TEF without atresia. We report the case of an infant born with TA and EA with proximal and distal
bronchoesophageal fistulas. During 3 consecutive antenatal ultrasound examinations, there had been
polyhydramniosis, difficulty visualizing the stomach, and dilatation of proximal esophagus, leading to a
presumptive diagnosis of EA. The clinical presentation, embryology, classification, and surgical
management are discussed.
Açıklama
Anahtar Kelimeler
Tracheal agenesis, Esophageal atresia, Prenatal diagnosis, Tracheoesophageal fistula, Bronchoesophageal fistula, Tracheal reconstruction
Kaynak
Journal of Pediatric Surgery
WoS Q Değeri
Scopus Q Değeri
Cilt
43
Sayı
Künye
Demircan, M. Aksoy, T. Ceran Özcan, C. Kafkaslı, A. (2008). Tracheal agenesis and esophageal atresia with proximal and distal bronchoesophageal fistulas. Journal of Pediatric Surgery. 43; E1-E3.
