An Epidermolysis Bullosa Patient Complicated with Chronic Renal Failure

Küçük Resim Yok

Tarih

2013

Dergi Başlığı

Dergi ISSN

Cilt Başlığı

Yayıncı

Galenos Yayincilik

Erişim Hakkı

info:eu-repo/semantics/openAccess

Özet

A 32-yr-old man with epidermolysis bullosa presented with clinical and laboratory findings of chronic renal failure. The patient was supposed to be suffering from mesangial IgA glomerulonephritis in view of the repeated persistent macroscopic episodes of hematuria and raised serum IgA levels, especially polimeric IgA. Because continuous vascular access could not be established, the patient died due to uremia and sepsis. Renal complications are associated with life-threatening problems in this inherited mechanobullous disease because it is impossible to obtain a continuous vascular access or a continuous peritoneal access. The possibility of IgA nephropathy should be considered in patients with epidermolysis bullosa. They should be periodically set up screened for IgA levels and hematuria.

Açıklama

Anahtar Kelimeler

Epidermolysis bullosa, kidney failure, chronic

Kaynak

Turk Dermatoloji Dergisi-Turkish Journal of Dermatology

WoS Q Değeri

N/A

Scopus Q Değeri

Q4

Cilt

7

Sayı

1

Künye