Intraabdominal lymphangiomyoma in an infant with protein-losing enteropathy and hemihypertrophy

Küçük Resim Yok

Tarih

2000

Dergi Başlığı

Dergi ISSN

Cilt Başlığı

Yayıncı

Turkish J Pediatrics

Erişim Hakkı

info:eu-repo/semantics/closedAccess

Özet

Lymphangiomyoma is an extremely rare tumor occurring exclusively in women of reproductive age. The tumor is characterized by proliferation of immature smooth muscle along the lymphatic vessels of the abdomen, thorax and lung. Although lymphangiomyoma has been reported in a young girl and a girl infant, none has been reported in boys. We report herein a case of lympangiomyoma in a two-year-old boy. The unusual presentation in this patient was that the tumor arose from the small bowel mesentery without any evidence of lung involvement. The tumor was extirpated and lymphangiomyomatosis was confirmed pathologically.

Açıklama

Anahtar Kelimeler

lymphangiomyoma, protein-losing enteropathy, hemihypertrophy

Kaynak

Turkish Journal of Pediatrics

WoS Q Değeri

Q4

Scopus Q Değeri

Q3

Cilt

42

Sayı

4

Künye